Journal of Experimental and Clinical SurgeryJournal of Experimental and Clinical Surgery2070-478X2409-143XVoronezh State Medical University132610.18499/2070-478X-2020-13-1-51-54UnknownPalliative surgery of a patient with hypoplastic left heart syndrome and low body weight.SoynovIlya<p>PhD, Cardiovascular Surgeon of the Department of Congenital Heart Diseases, Senior Researcher, Center for New Surgical Technologies, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>i_soynov@mail.ruhttps://orcid.org/0000-0003-3691-2848OmelchenkoAlexander<p>PhD, Cardiovascular Surgeon of the Department of Congenital Heart Diseases, Senior Researcher, Center for New Surgical Technologies, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>a.y.omelchenko@mail.ruhttps://orcid.org/0000-0001-9564-755XKeylIrina<p>Cardiologist of the Department of Congenital Heart Diseases, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>i_kejl@meshalkin.ruhttps://orcid.org/0000-0001-6691-0670LeykekhmanAnastasiya<p>Cardiologist of the Department of Congenital Heart Diseases, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>A_lejkekhman@meshalkin.ruhttps://orcid.org/0000-0001-9108-7153ChaschinOleg<p>PhD, Cardiovascular Surgeon of the Department of Congenital Heart Diseases, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>O_chaschin@meshalkin.ruhttps://orcid.org/0000-0001-8780-0374GalstyanMeline<p>Cardiovascular Surgeon Resident of the Department of Congenital Heart Diseases, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>melinegamletovna@yandex.ruhttps://orcid.org/0000-0003-3870-169XGorbatykhYuriy<p>PhD, Professor, Cardiovascular Surgeon of the Department of Congenital Heart Diseases, Leading Researcher, Center for New Surgical Technologies, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>YNG@meshalkin.ruhttps://orcid.org/0000-0002-6204-5381ArkhipovAlexey<p>PhD, Cardiovascular Surgeon, Head of the Department of Congenital Heart Diseases, Senior Researcher, Center for New Surgical Technologies, E.N. Meshalkin National Medical Research Center, Novosibirsk, Russian Federation.</p>a_arkhipov@meshalkin.ruhttps://orcid.org/0000-0003-3234-5436Meshalkin National Medical Research Center Ministry of Health Russian Federation25022020131515416042019Copyright © 2020, Soynov I., Omelchenko A., Keyl I., Leykekhman A., Chaschin O., Galstyan M., Gorbatykh Y., Arkhipov A.2020<p>Hypoplastic left heart syndrome is a congenital heart disease that affects the normal blood flow through the heart and it characterized by a critical underdevelopment of the left heart. Hypoplastic left heart syndrome is 1.43.8% among all congenital heart defects and 16% among critical congenital heart disease. Mortality in large cardiac surgery centers currently does not exceed 15%. However, mortality among patients with low body mass is up to 51% after the first stage of palliative surgery. In our clinical case, we describe hemodynamic surgery in neonatal with left-heart hypoplasia syndrome and low body weight (Norwood procedure with Sano shunt), postoperative case management inter-stage period and bidirectional cavopulmonary anastomosis procedure (second stage of hemodynamic correction).</p>Hypoplastic left heart syndrome, Norwood procedure, bidirectional cavopulmonary anastomosis procedure.Синдром гипоплазии левых отделов сердца, процедура Norwood, двунаправленный кавопульмональный анастомоз.[1. Hirsch JC, Gurney JG, Donohue JE, Gebremariam A, Bove EL, Ohye RG. Hospital mortality for Norwood and arterial switch operations as a function of institutional volume. Pediatr Cardiol 2008;29:713–7 (https://link.springer.com/article/10.1007%2Fs00246-007-9171-2)][2. Matyushov V.N., Sinel'nikov YU.S., Sojnov I.A., Kornilov I.A., Prohorov S.N., CHashchin O.V., Ivancov S.M. Analiz opyta hirurgicheskogo lecheniya obshchego arterial'nogo stvola. 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